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2012, Number 3

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Rev Cubana Hematol Inmunol Hemoter 2012; 28 (3)

Rendú-Osler-Weber disease: apropos of 5 cases with recurrent epistaxis

Alcalá-Villalón T, Castillo-González D, Agramonte-Llanes O

Language: Spanish
References: 30
Page: 289-298
PDF size: 107.85 Kb.


ABSTRACT

Patients with epistaxis represent 10 to 12 % of cases were seen at the emergency otolaryngology services. Five patients treated in this service at the General Teaching Hospital "Enrique Cabrera" from January 2010 to February 2011 were referred from the hematology service of this hospital due to episodes of spontaneous and recurrent epistaxis and family history of nasal bleeding. All of them had Rendu-Osler-Weber disease or hereditary hemorrhagic telangiectasia. We hereby describe the behavior of bleeding and present the association with platelet function disorders in two of them. The results of treatment and monitoring to control nosebleeds were satisfactory in all 5 cases.


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