Téllez-Olvera A, Romero-Álvarez J, Salgado-Molina MÁ

Language: Spanish
References: 9
Page: 79-82
PDF size: 110.59 Kb.

ABSTRACT

Objective: to report a case of Poland syndrome in a 67-year-old woman.
Clinical case: the patient was questioned and examined for a history of malformations characteristic of this syndrome on a routine medical visit. Thorax, bone thorax, and comparative hand X-ray were taken. Mammary ultrasound, mastography, and computed axial tomography were taken also. The right hemithorax showed a thin subcutaneous cell tissue. Axillary alopecia, mammary hypoplasia and areola-nipple complex retraction, hypoplasia of major pectoral muscles was observed. In the right upper limb, there was forearm shortening, hypoplasia of the second phalanx in all five fingers, and absence of distal phalanx in the index finger.
Conclusions: the patient showed 4 out of the 5 characteristics considered as typical by Hester and Bostwick. In terms of hand anomalies, she was classified as type 1 according to Gausewitz and according with Al-Qaifan, the patient belongs to type 2.

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