García-Aranda A, García-Torres CD, Sánchez-Medina F

Language: Spanish
References: 20
Page: 455-458
PDF size: 68.58 Kb.

ABSTRACT

Von Recklinghausen described de first rhabdomyoma in 1862. These tumors are considered benign due to their morphologic features; however, they can be the source of many clinical findings, rendering them a diagnostic challenge for the physician. Rhabdomyoma is the most frequent cardiac neoplasm of childhood. The majority of children with cardiac rhabdomyoma also have tuberous sclerosis, characterized by mental retardation, epilepsy, and adenoma sebaceum; it is uncommon in healthy adult population. Until the 1950s, cardiac tumors were merely a curiosity. Diagnosis was academic and of autopsy-related. More recently, development of cardiopulmonary bypass and invasive and non-invasive diagnostic technology has contributed greatly to the process of preoperative diagnosis. We describe here a previously healthy women who presented with heart and renal failure resulting from right atrium cardiac rhabdomyoma.

REFERENCES

1. Reece IJ, Cooley DA. Cardiac tumors. Clinical spectrum and prognosis of lesions other than classical benign mixoma in 20 patients. J Thorac Cardiovasc Surg 1984;88:439.

2. Gamallo C, Calvo de Mora J. Tumores cardíacos, antecedentes históricos, embriología, clasificación e incidencia. Departamento de Anatomía Patológica del Hospital La Paz, Madrid. Available at: http://www.castellanacardio.es/page2a6.htm

3. Fischer BR, Beerman LD. Diagnosis of intracardiac rhabdomyoma by two dimensional echocardiography. Am J Cardiol 1984;53:978-997.

4. Wilson SC, Schoen FJ. Primary tumors of the heart. In: Braunwald E, editor. Heart disease: a testbook of cardiovascular medicine. 5th ed. Philadelphia, PA, USA: W.B. Saunders Co.; 1997.pp.1464-1477.

5. Fenoglio JJ, MacCalister HA, Ferrans VJ. Cardiac rhabdomyoma, a clinicopathologic and electron microscopic study. Am J Cardiol 1976;38:241-250.

6. Fenoglio JJ, Diana DJ, Bowen TE. Ultrastructure of a cardiac rhabdomyoma. Hum Pathol 1977;8:700.

7. Hou WJ, Wang PJ, Wang TR. Tuberous sclerosis in children. Acta Paediatr Sin 1994;35:102-107.

8. Sagar SM, Israel MA. Tumores del sistema nervioso. In: Fauci AS, Braunwald E, editors. Harrison Medicina interna. 14th ed. Madrid, Spain: McGraw-Hill Interamericana;1998.pp.2731-2743.

9. Nadas AS, Ellison RC. Cardiac tumors in infancy. Am J Cardiol 1968;21:363-368.

10. Kuehl KS, Perry LW, Chandra R. Left ventricular rhabdomyoma: a rare cause of subaortic stenosis in the newborn infant. Pediatrics 1970;46:464.

11. Sharrat GP, Lacson AG, Cornel G. Echocardiography of intracardiac filling defects in infant and children. Pediatr Cardiol 1986;7:189.

12. Smythe JF, Dyck JD. Natural history of cardiac rhabdomyoma in infancy and childhood. Am J Cardiol 1990;66:1247-1249.

13. Wha J, Ward C, Nunn G. Primary intraventricular cardiac tumors in children: contemporary diagnostic and management options. Pediatr Cardiol 1994;15:233-237.

14. Jacobs JP, Konstantakos AK, Holland FW. Surgical treatment for cardiac rhabdomyomas in children. Ann Thorac Surg 1994;58:1552-1555.

15. Cooley DA. Surgical treatment of cardiac neoplasms. 32 years experience. Thorac Cardiovasc Surg 1990;38(Suppl 2): 176-182.

16. Farooki ZQ, Ross RD, Paridon SM. Spontaneous regression of cardiac rhabdomyoma. Am J Cardiol 1991;67:897-899.

17. Alkalay AL, Ferry DA, Lin B. Spontaneous regression of cardiac rhabdomyoma in tuberous sclerosis. Clin Pediatr 1987;26:532-535.

18. Chávez RI. Cardiopatías y tumores. In: Chávez RI, Puech P, Pileggi F, editors. Cardiología. México D.F: Editorial Médica Panamericana; 1993.pp.1319-1323.

19. Krasuski RA, Hesselson AB. Landolfo KP. Cardiac rhabdomyoma in an adult patient presenting with ventricular arrhythmia. Chest 2000;118(4):1217-1221.

20. Shapiro LM. Cardiac tumors: diagnosis and management. Heart 2001;85:218.