Solórzano MSA, Patiño GJL, Gil CF, Carrasco DD, Valdez DG

Language: Spanish
References: 16
Page: 201-208
PDF size: 499.71 Kb.

ABSTRACT

Introduction: The cystic adenomatoid malformation is a lung illness characterized by the proliferation of the respiratory epithelium in the terminal bronchioles followed by the formation of cysts.
Introduction of the case: Four days old infant. He was born in the Instituto Nacional de Perinatología (Perinatology National Institute) and was transferred to the Instituto Nacional de Pediatría (National Institute of Pediatrics) for diagnosis and treatment. It was product of a normal pregnancy. In the 36^th gestational week, a bilobate cystic tumor in the right hemithorax was discovered by ultrasound. It was thought that it was one of the following pathologies: congenital diaphragmatic hernia, broncogenic cyst or cystic adenomatoid malformation.
The X-ray in thorax showed a rounded opacity in the right hemithorax displacing the mediastinum structures, the ultrasound, show a multicameral cystic mass, CAT enabled dimensions evaluation, the presence of hydroaerial levels, the relationship with the adjacent parenchima lung and with the tracheobronchial tree.
Discussion: The cystic adenomatoid malformation in lungs (CAML), happens in one from each 5,000 to 20,000 born alive. The correct diagnosis allows giving a specific and timely treatment. The present case corresponds to A type 1CAML.

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