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2004, Number 2

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Rev Med UV 2004; 4 (2)

Ictiosis

Rodríguez GR, Román AR, Izquierdo MJA

Language: Spanish
References: 24
Page: 16-20
PDF size: 391.74 Kb.


ABSTRACT

Introduction. Ichthyosis is a group of illnesses that produces visible scales on all or a great part of the surface of the skin. Autosomal recessive ichthyosis is characterized by dry skin, desquamation of scales, and hyperkeratosis. The unpleasant appearance of this illness generates psychological disorder in the patients.
Cases. Two cases clinical cases of autosomal recessive ichthyosis are described one in a child and another in a young boy from the municipality of Ixhuatlán del Sureste, Veracruz. (The genealogical trees) are characterized with autosomal recessive ichthyosis illnesses. The most common clinical manifestations were ectropion, epiphora, eclabium, hyperkeratosic lesions in all the body. One patient has lost the right eye due to an ocular infection.
Conclusions. The autosomal recessive ichthyosis is an illness that is observed with certain frequency in this region. These two cases are added to the other four cases that had been previously reported in Veracruz. At present there is no treatment to cure this illness, there is only palliative treatment.


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