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Instituto Nacional de Neurología y Neurocirugía

2008, Number 2

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Arch Neurocien 2008; 13 (2)

Marchiafava-Bignami disease

Reyes SG, Mendizábal GR, Acosta GR, Ayala AA, Félix EI, Delgado HC, Monroy SA

Language: Spanish
References: 31
Page: 138-142
PDF size: 181.81 Kb.


ABSTRACT

Marchiafava-Bignami disease is characterized by demyelination of the callous body. The clinical features are varied, the most frequent symptoms being: dementia, attention disorders, gait difficulty and interhemispheric deconnection syndrome. Report case: We report a 69-year-old alcoholic man who presented with mental impairment. MRI, suggestive of corpus callosum demyelination with associated white matter involvement in left cerebral hemisphere and pons. Biopsy reveled demyelination and no evidence of tumor. The diagnosis of Marchiafava-Bignami disease was confirmed. Conclusions: this case raises questions about some previous ideas on this disease, such as the prognosis of its acute forms and the significance of the extracallosal lesions seen on neuroimaging.


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