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Colegio de Medicina Interna de México.

2010, Number 1

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Med Int Mex 2010; 26 (1)

Vasculitis retiniana y glomerulonefritis extracapilar pauci inmune como manifestaciones de inicio en el síndrome de Churg Strauss ANCA negativo.

Hernández SJC, Garzón GA, Solano RA, Varela GJA

Language: Spanish
References: 11
Page: 70-74
PDF size: 233.60 Kb.


ABSTRACT

The renal failure in the Churg Strauss syndrome has been described in the 16% of the patients, finding the tubulo-interstitial way as the most common (89%) and the focal and segmentary glomerulonephritis and rapidly progressive glomerulonephritis as unusual ways (5%). From the patients with renal failure, the 1% doesn’t present positive antibodies to neutrophil cytoplasmic antigens (ANCAs). The glomerulonephritis fast progressive pauci immune type is presented by the active nephritis and quick and progressive loss in days or months of the kidney function, indeed require substitute therapy. The prognosis is uncertain and it´s based and the answer to the immunosupressor treatment. We present a case about a patient with Churg-Strauss syndrome that appeared with visual affection and renal failure, showing retinal vasculitis and rapidly progressive glomerulonephitis, negative ANCAs that had a bad response to the immunosupressor schema whit steroids and biological agents.


REFERENCES

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