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Anales de la Sociedad Mexicana de Oftalmología y Archivos de la Asociación Para Evitar la Ceguera en México

2009, Number 4

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Rev Mex Oftalmol 2009; 83 (4)

Alteraciones oculares en síndrome de Marfan: Revisión de 130 casos

Figueroa-Magaña BB, Salcedo-Villanueva G, Villanueva-Mendoza MC

Language: Spanish
References: 26
Page: 201-205
PDF size: 93.92 Kb.


ABSTRACT

Objective: To determine the most common ocular alterations in patients with Marfan’s syndrome.
Methods: Observational, retrospective and longitudinal study. One hundred and thirty files of patients with Marfan’s syndrome were reviewed. The characteristics of the anterior and posterior segment, keratometries and antero-posterior axis by ultrasound were determined.
Results: Ectopia lentis was found in 87.7% of the patients, retinal degeneration was found in 21.4% and rhegmatogenous retinal detachment in 22.4%. Other important findings were flat corneas and an increase in the length of the anteroposterior axis.
Conclusions: Ectopia lentis constitutes major criteria for the diagnosis of Marfan’s syndrome. However, the ophthalmologist must know other ocular alterations also present in the disease for an accurate diagnosis as for the prevention of complications.


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