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2005, Number 2

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Rev Med Hosp Gen Mex 2005; 68 (2)

Peutz-Jeghers syndrome

Abdo FJM, Pérez TE, Bernal SF, Dzib SJ

Language: Spanish
References: 28
Page: 99-105
PDF size: 99.25 Kb.


ABSTRACT

The Peutz-Jeghers syndrome is an uncommon autosomic predominant hereditary entity which main characteristics are the mucocutaneous pigmentation, associated to hamartomatosis polyps. In this paper we made a critical review of the item and the relation with cancer of the digestive tract and of extraintestinal locations.
The screening protocol and treatment are analyzed.


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