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2005, Número 2

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Rev Med Hosp Gen Mex 2005; 68 (2)


Síndrome de Peutz-Jeghers

Abdo FJM, Pérez TE, Bernal SF, Dzib SJ

Idioma: Español
Referencias bibliográficas: 28
Paginas: 99-105
Archivo PDF: 99.25 Kb.


RESUMEN

El síndrome de Peutz-Jeghers es una entidad hereditaria autosómica dominante poco común. Se caracteriza por la presencia de pigmentación mucocutánea asociada a pólipos hamartomatosos. Se revisa el tema y su relación con cáncer del tubo digestivo y de localización extraintestinal.
Se analiza el protocolo de vigilancia y de tratamiento


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