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Medicina Universitaria

2007, Number 37

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Med Univer 2007; 9 (37)

Cystic adenomatoid malformation in a 2-month-old Mexican infant. Case report and review of the literature

Díaz VA, Chapa RA, Villarreal E, Chapa-Rodríguez A, Jaime PJC

Language: English
References: 22
Page: 203-207
PDF size: 150.03 Kb.


ABSTRACT

Background: Congenital cystic adenomatoid malformation (CCAM) is a multicystic hamartomatous abnormality of lung tissue that involves the distal airway. It represents 25% of all congenital lung malformations.
Case report: We describe the case of a 2 month old female referred with a presumptive diagnosis of lower respiratory tract infection and positive tuberculosis exposure. The patient was delivered by cesarean section after an uneventful pregnancy with adequate weight and height for gestational age. The child was breast fed with formula supplementation; psychomotor development was unremarkable. Her immunizations were up to date; her mother has an unspecified collagen disease. Physical examination and laboratory tests were unremarkable. Chest X-ray and CT scan revealed a moderately radiopaque thick walled mass with well defined borders located in the right lower lobe with three radiolucid circles in its interior. The intercostal spaces were enlarged, the heart and mediastinum displaced to the right. The patient underwent a right upper lobectomy. Pathology reported a type I CCAM.
Conclusion: Prenatal screening and proper diagnosis are vital for a positive outcome. Although a rare pathology, it is important for physicians to consider the diagnosis each time they perform an ultrasound on a pregnant patient. Our patient’s recovery was uneventful.


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