2007, Number 4
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Otorrinolaringología 2007; 52 (4)
Type I neurofibromatosis affecting external ear: case report
Waizel HS, Aponte RHX, Vargas AAM, Monter CGA
Language: Spanish
References: 19
Page: 159-164
PDF size: 242.54 Kb.
ABSTRACT
We present the case of a 20 year old woman; with a 15 year history of a slowly enlarging, painless, soft tissue mass of the right external auditory canal and ear, and a two year history of progressive hearing loss. The external auditory canal was partially obstructed by a subcutaneous thickening. The tympanic membrane was normal. Results of cranial nerve examination were normal. In this particular patient we decided for conservative treatment with periodic followup, because the neurofibroma was not causing significant symptoms, functional impairment or neurological deficit, and there is no evidence of malignant degeneration.
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