Franco-Díaz de León A, Rodríguez-Reyes AA, Gómez-Leal A

Language: Spanish
References: 8
Page: 48-51
PDF size: 519.11 Kb.

ABSTRACT

Objective. To report the 44 year experience at the Asociación para Evitar la Ceguera en México, IAP., Hospital "Dr. Luis Sánchez Bulnes" of cases with clinic and pathologic diagnosis of primary gelatinous drop-like dystrophy
Material and methods. A retrospective, descriptive, observational study of familiar and isolated cases with diagnosis of primary gelatinous drop-like dystrophy, from august 1957 to July 2001, at the Hospital. The main clinical and histopathological findings of all cases were analysed.
Results. In eighteen corneas from 13 patients with diagnosis of primary gelatinous drop-like dystrophy, the mean age was 19 years, with slight preponderance for male gender. The clinical diagnosis of primary gelatinous drop-like dystrophy was done in all cases. Six of 13 patients had recurrences. History of involvement in more than one relative of the same family was present in eight patients. Bilateral surgery was performed in 2 patients.
Conclusions. To the best of our knowledge, this is the largest series documented in the literature. The clinical and histopathological characteristics of this series are similar to those previously reported in the literature.
History of the disease in more than one relative of the same family as well as involvement of both eyes, were more frequent in our series in contrast to other previously reported in the literature. The number of recurrences was greater in the current study than in other series reported. The histopathology study is necessary to support the diagnosis of primary gelatinous drop-like dystrophy.

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