Estrada MM, Guerrero AGML, Enríquez GR, González de la CJ

Language: Spanish
References: 16
Page: 245-251
PDF size: 157.52 Kb.

ABSTRACT

Introduction: The Klippel Trenaunay syndrome (KT) it is a rare mesodermal congenital disturbance, present at birth, that is manifested in the childhood or adolescence, of unknown etiology and of variable expression. It is characterized by cutaneous hemangiomas that can embrace almost the whole body, they can show vascular malformations, bony or soft tissues hypertrophy, which can be uni- or bilateral. For an appropriate diagnostic, imaging techniques will help us to the patient’s integral handling.
Objective: Our objective intends to show the clinical aspects and the imaging findings including the (US) Doppler color in this less frequent disease.
Method and materials: The clinical-radiological case of a 12 year-old male patient was shown, who manifested “fatigue, heaviness and pain” in the right pelvic member, besides showing a wine light colored macular stain of not well defined irregular borders that corresponds to a hemangioma in hemi-face, hemi-torax and that continues up to the superior and inferior limb of the right side, which is congenital. He was submitted to flebography with tourniquets in both legs and thighs, those which were insufflated to a pressure of 130 mm Hg, the fluoroscopy equipment used was a Prestige II from GE. Doppler ultrasound in both pelvic members and abdominal ultrasound, were carried out with a SIEMENS Acuson Antares equipment with 3.6 MHZ convex transducer for the abdominal ultrasound and of 7-3 MHZ for the color Doppler ultrasound and ortho-measurement. The film used in all the studies is Kodak Laser Dryview Imaging.
Discussion and conclusion: Hypertrophy of the MPD, difference of iliac crests height was demonstrated and in the ortho-measurement a differential value of 3.4 cm, was obtained; an abnormal development in the deep venous system in the right pelvic member was observed, especially of the communicating veins. This patient’s prognosis with Klippel-Trenaunay syndrome will be subject to the affecting degree and the presence of later complications, for which in some patients perhaps they will only need symptomatic treatment. The relevance of this article resides in the clinical diagnosis and in findings found in the imaging studies, to provide our patients an opportune treatment and to avoid further complications.

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