Fuentes-Mallozzi DA, Cortés-Cruz JA

Language: Spanish
References: 18
Page: 70-73
PDF size: 229.05 Kb.

ABSTRACT

Introduction. The Cantrell’s Pentalogy is an uncommon syndrome constituted by different congenital malformations of the body’s midline. Include: 1) defect of the lower part of sternum, 2) diaphragm ventral defect, 3) pericardium defect, 4) abdominal wall defect (omphalocele) and 5) cardiac anomalies. Case report. Female, full-term new born, 40 weeks by Capurro, with normal parents, with the complete presentation of Cantrell’s pentalogy. She lived for 32 days until she died by cardiac insufficiency. Conclusions. There are a few cases reported with good outcome, the prognosis will depend of the cardiac anomalies. But, for a good outcome we must have a complete medical team including pediatrics, neonatology, cardiology, pediatric surgeons and cardiovascular surgeons besides of the medical technology.

REFERENCES

1. Vázquez-Jiménez JF, et al. Cantrell’s syndrome: a challenge to the surgeon. Ann Thorac Surg 1998; 65: 1178-85.

2. Mendoza-García BP, Durán-Padilla MA, Reséndiz-Morán MA. Síndrome de bandas amnióticas asociado a malformaciones de la pentalogía de Cantrell. Rev Mex Pediatr 2004; 71: 286-8.

3. Oka T, et al. Usefulness of helical CT angiography and MRI in the diagnosis and treatment of pentalogy of Cantrell. J Pediatr 2003; 142: 84.

4. Song A, McLeary MS. MR imaging of Pentalogy of Cantrell variant with intact diaphragm and pericardium. Pediatr Radiol 2000; 30: 638-9.

5. Önderoðlu L, et al. Prenatal diagnosis of Cantrell’s pentalogy: a case report. Turk J Pediatr 2003; 45: 357-8.

6. Soria-López JA, et al. Presentación y discusión de un paciente con Pentalogía de Cantrell. Rev Cubana Obstet Ginecol 2004; 30: 1-4.

7. Bittmann S, Ulus H, Springer A. Combined pentalogy of Cantrell with Tetralogy of Fallot, gallbladder agenesis and polysplenia: a case report. J Pediatr Surg 2004; 39: 107-9.

8. Cortés H, Vélez F. Diagnóstico ecográfico prenatal de la pentalogía de Cantrell. Rev Colomb Gine Obst 2003; 53: 1-4.

9. Bognoni V, Quartuccio A, Quartuccio A. First-trimester sonographic diagnosis of Cantrell’s pentalogy with excencephaly. J Clin Ultrasound 1999; 27: 276-8.

10. Yadav P, Mukherjee S, Sikarwar JS, Gupta RP. Case report: Cantrell’s pentalogy associated with encephalocele – A prenatal second trimestre sonographic diagnosis. Ind J Radiol Imag 2003; 13: 145-6.

11. Morales JM, et al. Ectopia cordis and other midline defects. Ann Thorac Surg 2000; 70: 111-14.

12. García H, Franco-Gutiérrez M, Chávez-Aguilar R, et al. Morbilidad y mortalidad en recién nacidos con defectos de pared abdominal anterior (onfalocele y gastrosquisis). Gac Med Mex 2002: 138; 519-26.

13. Nanda S, et al. Cantrell’s syndrome: report of two cases with one atypical variant. Arch Gynecol Obstet 2003; 268: 331-2.

14. Begum H, Nayek K. Cantrell’s Pentalogy. Indian Pediatrics 2002; 39: 501.

15. Falcão-Araripe JLA, et al. Síndrome de Cantrell. Relato de caso em Adulto. Arq Bras Cardiol 2000; 75: 323-5.

16. Agrawal N, Sehgal R, Kumar R, Bhadoria P. Cantrell’s pentalogy. Anaesth Intensive Care 2003; 31: 120-3.

17. Yazicioglu HF, et al. Pentalogy of Cantrell: two more cases. Ultr Obstet Gynecol 2003; 22(Suppl. 1): 111.

18. Gómez-Osako MG, Bautista-Vázquez A, Prats-Suárez A, Vázquez-Camacho G. Pentalogía de Cantrell. Reporte de un Caso. Bol Med Hosp Infant Mex 2003; 60: S 35.