2024, Number 1
Congenital Methemoglobinemia. A case report
Gutiérrez-Riverol K, Lozada RKG, Herrera JD, Avelar AC
Language: Spanish
References: 5
Page: 17-21
PDF size: 291.32 Kb.
ABSTRACT
Methemoglobinemia occasionally causes cyanosis particularly in congenital methemoglobinemia. Avoidance of exposure to oxidizing agents is important for patients with congenital methemoglobinemia because of their deficient enzymatic pathways and decreased oxygen-carrying capacity. Here, we present a pediatric patient with preoperatively undiagnosed congenital methemoglobinemia who underwent catheterization with probably diagnosis of pulmonar hypertension under general anesthesia. The pediatric patient was a 10-year-old who displayed a low pulse oximetry reading of 92% prior to induction of anesthesia. Methemoglobinemia was first suspected intraoperatively because of a mismatch of SpO2 of finger pulse oximetry and SaO2 of arterial blood, and was later confirmed by multiplewavelength CO-oximetry. The pathophysiology, etiology, clinical manifestations, anesthetic considerations, and treatment options of methemoglobinemia are discussed.REFERENCES
Quiñones Coneo KL, Carvajal del Castillo O, Bello GutiérrezP, Pulido Ovalle E, Caro Gutiérrez MD. Metahemoglobinemiasecundaria a aplicación de un anestésico tópico(EMLA). Rev Pediatr Aten Primaria [Internet]. 2021 Mar[citado 2023 Mayo 31];23(89):79-81. Epub 09-Mayo-2022.Disponible en: http://scielo.isciii.es/scielo.php?script=sci_arttext&pid=S1139-76322021000100012&lng=es