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2022, Number 3

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Acta Pediatr Mex 2022; 43 (3)

Craniosynostosis: literature review

Ocampo-Navia MI, Alvarez-García D, Gempeler A, Velásquez F

Language: Spanish
References: 74
Page: 179-192
PDF size: 363.67 Kb.


ABSTRACT

Craniosynostosis is the second most frequent type of craniofacial malformation; it is characterized by the premature closure of one or more skull sutures. It results in a change in skull morphology that restricts normal brain growth and development; with possible impaired cognitive development of the individual. It can be classified according to the etiology, the presence of other associated syndromic alterations and the number of affected sutures. Non-syndromic craniosynostosis represents 75% of the cases of this pathology, and the sagittal suture is the most affected. Its diagnosis is predominantly clinical and must be made early in order to provide timely treatment that allows normal brain development. The management of this pathology must be multidisciplinary. An updated non-systematic review on the epidemiology, classification, pathophysiology, diagnostic and therapeutic approach of craniosynostosis is presented.


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