Durán PMA, Rivero JV, Macías JB

Language: Spanish
References: 14
Page: 206-209
PDF size: 210.50 Kb.

ABSTRACT

Two cases of the lethal variant of syndrome Prune Belly are described in which urethral obstruction produced serious alterations with vesical and ureteral distension with secondary repercussion on the abdominal wall and renal bilateral dysplasia. The theories of the etiopathogeny of this syndrome are commented, those of the mesoderm development alteration of the early obstruction of the urethral that caused abdominal wall malformation. In the two cases, the severity of urinary tract obstruction produced lethal development malformations.

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