Martínez-Domingo R, Bravo-Arribas C, Gámez-Alderete F, García de Castro-Rubio E, De León LJ

Idioma: Español
Referencias bibliográficas: 28
Paginas: 738-742
Archivo PDF: 436.93 Kb.

RESUMEN

El drenaje venoso pulmonar anómalo es un padecimiento raro en sus formas parciales o totales, descritas según el número de venas pulmonares que drenen en la aurícula izquierda. En las formas totales se distinguen cuatro grupos, dependiendo del lugar en el que drenen las venas pulmonares: supra, intra o infra-cardiacas y, finalmente, una forma mixta menos frecuente. Es una cardiopatía de difícil diagnóstico prenatal e, incluso, postnatal, sobre todo en las formas parciales sin otras anomalías. La asociación con cromosomopatías es baja; sin embargo, está estrechamente vinculada con malformaciones cardiacas complejas, sobre todo en el contexto de síndromes heterotáxicos, casi siempre en las formas totales, lo que ensombrece el pronóstico perinatal.
Se comunica el caso de un paciente con drenaje venoso pulmonar anómalo total infracardiaco, en el contexto de una cardiopatía compleja, asociada con canal auriculoventricular completo y anomalía conotruncal, operado a las 48 horas de vida con mala evolución posterior. Se describen las características ecográficas y de angiorresonancia de esta anomalía y su pronóstico y tratamiento perinatal.

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