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2009, Número 6

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Rev Med Inst Mex Seguro Soc 2009; 47 (6)


Síndrome de Marfán, aneurisma toracoabdominal disecado y embarazo. Informe de un caso

Mendoza-Álvarez SA, Fuentes-León J, Vargas-Ayala G, Hernández-González C, López-Arias G, Vera-Lastra O

Idioma: Español
Referencias bibliográficas: 21
Paginas: 669-672
Archivo PDF: 93.84 Kb.


RESUMEN

Paciente de 39 años con diagnóstico de síndrome de Marfán y aneurisma toracoabdominal desde dos años atrás, manifestado por disnea de medianos esfuerzos y dolor torácico ocasionales. Inició padecimiento actual a las 28 semanas de gestación con exacerbación del dolor torácico, transfictivo, opresivo y ortopnea. El ecocardiograma mostró aneurisma aórtico de 10 cm de diámetro con afección del cayado aórtico, aorta toracoabdominal y disección; y la tomografía computarizada, dilatación aneurismática del cayado de la aorta y disección de la porción torácico-abdominal. La paciente fue tratada en forma exitosa con metoprolol, prazocin, diurético y cesárea a las 29 semanas.


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