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Boletín Médico del Hospital Infantil de México

2010, Número 2

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Bol Med Hosp Infant Mex 2010; 67 (2)


Tumor sólido pseudopapilar del páncreas pediátrico. Presentación de un caso y revisión en la literatura

Camacho AJF, Duarte VJC, Hidalgo CJF, Valenzuela EA, Ortíz EP

Idioma: Español
Referencias bibliográficas: 51
Paginas: 133-141
Archivo PDF: 214.93 Kb.


RESUMEN

Introducción. El tumor sólido pseudopapilar del páncreas (TSP) es un tumor epitelial de baja malignidad que afecta principalmente a mujeres jóvenes y comprende aproximadamente 1-2% de todas las neoplasias de páncreas. Presentamos un caso de este tipo de tumor tratado en el Hospital General de Tijuana en el Servicio de Cirugía Pediátrica, así como una revisión de la literatura.
Caso clínico. Se presenta el caso de un paciente femenino de 12 años de edad con la única sintomatología de tumor palpable en epigastrio de crecimiento progresivo. Es diagnosticada con un tumor sólido pseudopapilar localizado en la cola del páncreas y tratada exitosamente con pancreatectomía distal sin esplenectomía. Se egresa a los 3 días de postquirúrgico.
Discusión. Se concluye que el TSP es un diagnóstico diferencial ante la presencia de masas a nivel del páncreas, aunque por su rareza no debe ser la primera opción a descartar, especialmente en pacientes pediátricos. La cirugía por sí sola representa el mejor tratamiento para esta entidad patológica, ya que demuestra un nivel de curación excelente, y se debe intentar en todos los casos independientemente del tamaño de la lesión pancreática.


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