2006, Number 6
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Acta Ortop Mex 2006; 20 (6)
Chondroid chordoma of the cervical spine. Case report
Cardoso MA, Rosales MME, González AOC
Language: Spanish
References: 13
Page: 276-283
PDF size: 322.67 Kb.
ABSTRACT
Introduction. Chordoma is a malignant tumor that results from remnants of the primitive notochord. It has predilection for patients in their fifties to seventies; however, cases at all ages have been reported. Two treatment modalities are usually considered: surgical, consisting of en-bloc resection, and radiotherapy.
Case report. Female, 16-year-old patient, with forced dorsal decubitus attitude, intense neck pain and left otalgia; clinical and radiological diagnosis of C2 extradural intra- and extra-cordal tumor. The biopsy report stated chondroid chordoma. The tumor was resected using an anterior and posterior approach, broadening of the foramen magnum, performing C1-C2-C3 arthrodesis and posterior instrumentation with a Luque rod from the skull to C6.
Discussion. There are only a few reports of chondroid chondroma in pediatric ages in the world literature. Even though “en-block” resection is the recommended treatment, this was not possible due to the anatomical particularities of the region involved. Three surgical interventions were performed and complete tumor resection was achieved. At 15 months patient course has been appropriate, without motor or sensory deficit, and the oncologic follow-up shoes no recurrence of the lesion. The result of the work-up protocol and surgical treatment was satisfactory and we consider this as an appropriate treatment option.
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