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ISSN 2078-7170 (Electronic)

2020, Number 1

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CorSalud 2020; 12 (1)

Torsades de pointes in a patient with congenital long QT syndrome during the puerperium: Case report

Ravelo DR, Silva GML, Medina RG, Cruz RLO, Cárdenas FY, Yunez SP, Valdés CE

Language: Spanish
References: 17
Page: 93-98
PDF size: 463.14 Kb.


ABSTRACT

Congenital long QT syndrome is a primary electrical disorder of the heart which predisposes to the occurrence of malignant ventricular arrhythmias. It is characterized by a prolongation of the QT interval on the electrocardiogram and the torsade de pointes is the main associated arrhythmia, resulting in syncope and sudden cardiac death. Pregnancy and puerperium increase the incidence of those events. We present the case of a patient who suffered from this disorder, and during the post-delivery period, she had events of faint and anxiety interpreted as psychogenic. Torsades de pointes without response to the available antiarrhythmic drugs was documented and she was transferred to the reference center (Instituto de Cardiología y Cirugía Cardiovascular), where the pacemaker stimulation frequency was increased and, subsequently, an implantable cardioverter-defibrillator was implanted. This is an infrequent case that was a real challenge for the comprehensive and emergent treatment, all of which enabled the survival of the patient.


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