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2020, Number 1

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Rev Cubana Cardiol Cir Cardiovasc 2020; 26 (1)

Congenital diaphragmatic hernia of Bochdalek and left isomerism in a premature infant

Arias OY, Goire GG, Aguirre RAC, Fournier CG, Vazquez VRN, Bolivar VD

Language: Spanish
References: 20
Page: 1-6
PDF size: 225.89 Kb.


ABSTRACT

Congenital diaphragmatic hernia is a severe malformation with poor neonatal prognosis. It consists of a disorder in the development of the diaphragmatic muscle, producing the passage of abdominal content to the thoracic cavity. The main types are Bochdalek, Morgagni and hiatal hernia. Its incidence is one for every 2000-5000 live births and 50% of cases have other associated congenital anomalies, mainly cardiac. Prenatal ultrasound determines the diagnosis, prognosis and therapeutic of this condition. The surgery consists of closing the defect and correcting the intestinal malrotation, being the objective of the treatment to maintain an adequate gas exchange and avoid or minimize hypoplasia and pulmonary hypertension. We present a case of a premature newborn, with a diagnosis of congenital diaphragmatic hernia associated with left atrial isomerism.


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