2020, Number 03
Diagnosis and management of the catastrophic antiphospholipid syndrome
Language: Spanish
References: 21
Page: 394-394
PDF size: 134.19 Kb.
ABSTRACT
The antiphospholipid syndrome is a heterogeneous pathology with thrombotic, obstetric and non-thrombotic manifestations, associated with the presence of different antiphospholipid antibodies. Its catastrophic form is rare, in most cases it is related to a triggering factor and it manifests itself with the presence of multiple thrombi that can be lodged in any part of the body and that histologically appear as a thrombotic microangiopathy. This disease must be recognized in a timely manner for the immediate establishment of triple therapy, which decreases its mortality.REFERENCES
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Tektonidou MG, Andreoli L, Limper M, Amoura Z, Cervera R, Costedoat-Chalumeau N, Cuadrado MJ, Dörner T, Ferrer-Oliveras R, Hambly K, Khamashta MA, King J, Marchiori F, Meroni PL, Mosca M, Pengo V, Raio L, Ruiz-Irastorza G, Shoenfeld Y, Stojanovich L, Svenungsson E, Wahl D, Tincani A, Ward MM. EULAR recommendations for the management of antiphospholipid syndrome in adults. Annals of the Rheumatic Diseases. 2019 05 15;78(10):1296-1304. https://doi.org/10.1136/annrheumdis-2019-215213