2019, Number 5
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Cir Cir 2019; 87 (5)
Goldenhar syndrome: surgical management protocol in a reference center
Guevara-Valmaña OI, Nahas-Combina L, Andrade-Delgado L, Apellaniz-Campo AG, Leyva-Sotelo LM, Gaspar-Daniel Á
Language: Spanish
References: 20
Page: 516-527
PDF size: 612.55 Kb.
ABSTRACT
Objective: To present our experience treating 42 patients with Goldenhar syndrome.
Method: A descriptive, observational,
retrospective study was carried out using the medical and photographic record of all patients diagnosed with Goldenhar syndrome
treated by the craniofacial surgery unit of the plastic and reconstructive surgery department of the Dr. Manuel Gea
González hospital between 2010 and 2018.
Results: A total of 42 patients were obtained,54% male of which all underwent at
least one procedure. The majority of patients were of the first decade of age (57%). Surgical procedures could be divided
mainly into 14 auricular (20%), 17 mandibular (24%), 2 Lefort (4%), 10 volume (14%), 9 macrostoma (13%) and 16 other
(21%). A total of 71 procedures were performed.
Conclusion: Goldenhar syndrome is a rare entity that affects various structures,
which is why an early diagnosis and multidisciplinary management headed by a team of plastic surgeons is necessary.
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