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ISSN 1025-0255 (Electronic)

2019, Number 2

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AMC 2019; 23 (2)

Leiomyosarcoma of the superior vena cava with extension to the right heart cavities

García RME, Romay BR, Benavides MA, Ramírez RE, Toledo CY, Chávez CMA

Language: Spanish
References: 16
Page: 256-263
PDF size: 418.87 Kb.


ABSTRACT

Background: the leiomyosarcoma of the superior cava vein is a rare illness and more when it extends to the cardiac cavities.
Objective: to present to the medical community a female patient with leiomyosarcoma of the superior cava vein that extended intraluminal form to the right cavities of the heart causing obstruction and cardiogenic shock.
Clinical case: a 45-year-old white female patient with no morbid health history, who presented redness of the face and exhaustion of the extremities when combing. A computerized axial tomography was performed where a lesion suggestive of thrombosis was identified. It was decided to transfer her to a specialized center, in which it is concluded that the patient was a carrier of a non-thrombotic tumor lesion, which turned out to be benign in a biopsy done for which follow-up is decided. The patient reenters in a state of cardiogenic shock due to progression of the disease, which is why her emergency surgical treatment is decided and die during surgery.
Conclusions: the leiomyosarcoma of the superior vena cava is a rare illness, with few reports in the literature. A case in which the tumor extended intraluminally to the right cardiac cavities (atrium and ventricle) is presented.


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