Domínguez-Hernández HA, Gutiérrez-Alvarado RA, Peraza-McLiberty RA

Language: Spanish
References: 18
Page: 329-335
PDF size: 923.06 Kb.

ABSTRACT

Medulloblastoma is a relatively common tumor in children, accounting for 20% of primary tumors of the central nervous system in children; it has a tendency to spread along the neuroaxis through spinal fluid at the time of diagnosis. Metastasis is associated with poor prognosis and has mean survival of three to six months. Metastasis has been observed predominantly in the brainstem and only 0.6% affects the spinal cord. We present the case of a patient of 5 years of age who presented with progressive cephalea and ataxia of one month’s evolution; It was decided to take a single-phase computerized tomography of the skull, which found dilation of the ventricular system with tran sependymal migration of spinal fluid, for which reason the patient underwent emergency surgery to implant a peritoneal ventricular bypass valve. The patient was admitted to our unit to continue the study protocol, with magnetic resonance of encephalon and neuroaxis, with administration of gadolinium, identifying a space-occupying lesion in the cerebellum and leptomeningeal metastasis. The diagnosis was confirmed by medullary biopsy.

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