Pineda-Galindo LF, Vera-Lastra OL, Carrazco-Ibarra L, Carrasco-Gómez A, Becerril-Ángeles M, Ramos-Salazar P, Martínez-Solano J

Language: Spanish
References: 14
Page: 796-800
PDF size: 325.62 Kb.

ABSTRACT

IgG4-related disease is an inflammatory condition characterized by high levels of IgG4. It affects salivary and lacrimal glands, pancreas, lymph nodes, lungs or kidney. The diagnosis is based on identifying a histological pattern with a dense lymphocyte and plasmacyte infiltration, focal fibrosis or phlebitis, finding more than 10 IgG4 positive cells per high power field and/or IgG4/IgG ratio in plasma higher than 40%. We present a patient with M kulicz’s disease who meets histological findings required for the diagnosis of IgG4 related disease.

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