2016, Number 4
Prenatal rhabdomyomas. Case report
Language: Spanish
References: 12
Page: 618-625
PDF size: 184.61 Kb.
ABSTRACT
Introduction: Primary cardiac tumors are rare in childhood and mostly benign, being the most common rhabdomyomas, associating more than 60 % of patients with tuberous sclerosis. Most of them tend to regress, but some, depending on their location and clinical manifestations, require surgical treatment. Regardless of its benign character (it is considered a hamartoma and not a true neoplasm), their tendency sometimes to obstruction of tracts input or output, and heart Arrhythmogenesis, makes prognosis that is uncertain. Case report: pregnant 25.5 weeks of gestation with a history of previous health than in fetal echocardiography several cardiac tumors are identified in the left ventricle, septum and interventricular larger tumor in left ventricular (LV) outflow tract obstructing this. The case had followed for Clinical genetics for Rhabdomyoma obstructing the RV outflow tract. The patient decided the abortion and the diagnosis were confirmed by pathological examination. Conclusions: Fetal cardiac tumors are extremely rare. You can be diagnosed by ultrasound from intrauterine life. The recommended attitude is expectant about the possibility of spontaneous regression, except in cases with clinical impact. In the follow-up should rule out the presence of tuberous sclerosis because of its high association with this entity.REFERENCES
Sánchez Andrés A, Insa Albert B, Carrasco Moreno J, Cano Sánchez A, Moya Bonoza A, Sáez Palacios JM. Tumores cardíacos primarios en la infancia. An Pediatr (Barc) [internet]. 2008 [citado jul 2015];69(1):[aprox. 14 p. ]. Disponible en: http://www.analesdepediatria.org/es/tumores-cardiacos-primarios-infancia/articulo/S1695403308702327/
Arnaiz GP, Toledo G I, Borzutzky S A, Urcelay M G, Heusser R F, Garay G Francisco et al. Comportamiento clínico de los tumores cardíacos desde el feto hasta el adulto: serie multicéntrica de 38 pacientes. Rev Méd Chile [Internet]. 2006 [citado 30 jul 2015];134(9):[aprox. 23 p.]. Disponible en: http://www.scielo.cl/pdf/rmc/v134n9/art08.pdf
10.Savío Benavides A, Oliva Rodríguez J, García Morejón C, García Guevara C, Arencibia Faire J, Ponce Bittar J. Diagnóstico ecocardiográfico de los tumores primarios del corazón en el feto. Rev Cubana Ped [Internet]. 2009 [citado 25 Jun 2016];81(4): [aprox. 10 p.].Disponible en: http://www.bvs.sld.cu/revistas/ped/vol81_4_09/ped01409.htm
11.Paz Muñiz P de la, Ferreira Moreno V, Mesa Castellín A, Montes de Oca Rodríguez E, Peña Rodríguez O. Tumor cardíaco en la infancia. A propósito de un caso. Rev Méd Electr [Internet]. 2007 [citado 25 Jun 2016];29(2):[aprox. 3 p.]. Disponible en: http://www.revmedicaelectronica.sld.cu/index.php/rme/rt/captureCite/404/pdf