medigraphic.com
Organo Oficial de la Sociedad Mexicana de Urología

2005, Number 6

<< Back Next >>

Rev Mex Urol 2005; 65 (6)

Kidney angiomyolipoma, a multifacet entity. Five cases report

Gállego SS, Jamaica VE, Guerrero MJ, Zárate OA

Language: Spanish
References: 10
Page: 445-450
PDF size: 219.62 Kb.


ABSTRACT

The angiomyolipoma is a benign neoplasm that consist of varying amounts of mature adipose tissue, smooth muscle and thick-walled vessels. It has been found in 0.3% of autopsies and in 0.13% of the population when screened by ultrasonography. Approximately 20% are found in patients with tuberous sclerosis syndrome, disorder characterized by mental retardation, epilepsy and adenoma sebaceum. They can be discovered occasionally by abdominal ultrasound and seldom present symptoms that suggest the diagnosis. It exists the risk of spontaneous retroperitoneal bleeding in 10% of the cases. We present five cases with different clinic manifestations and the specific management for each one of them.


REFERENCES

  1. Steiner M, Goldman S, Fishman E, Marshal F. The natural history of renal angiomyolipoma. J Urol 1993; 150: 1782-6.

  2. MacCollin N, Kwiatkowski D. Molecular genetic aspects of the phakomatoses: tuberous sclerosis complex and neurofibromatosis 1. Current Opin Neurol 2001; 142: 163-9.

  3. Eble J. Angiomyolipoma of kidney. Semin Diagn Pathol 1998; 15: 21-40.

  4. Oesterling J, Fishman E, Goldman S, Marshall F. The management of renal angiomyolipoma. J Urol 1986; 135: 1121-4.

  5. Chan J, Tsang W, Pau M, Tang M, Pang S, Fletcher C. Lymphangiomyomatosis and angiomyolipoma: closely related entities characterized by hamartomatous proliferation of HMB-45 positive smooth muscle. Histopathology 1993; 22: 445-55.

  6. Juu J, Lu C, Pern R. Tuberous sclerosis associated with pulmonary lymphangioleiomyomatosis. Zhonghua Yi Xue Za Zhi 1991; 47: 65-70.

  7. Delgado R, De León B, Albores J. Atypical angiomyolipoma of the kidney; a distint morphologic variant that is easily confused with a variety of malignant neoplasms. Cancer 1998; 83: 1581-92.

  8. Kawaguchi K, Oda Y, Nakanishi K, Saito T, Tamiya S, et al. Malignant transformation of renal angiomyolipoma. A case report. Am J Surg Pathol 2002; 26: 523-9.

  9. Eble H, Amin M, Young R. Epithelioid angiomyolipoma of the kidney: a report of five cases with a prominent and diagnostically confusing epithelioid smooth muscle component. Am J Surg Pathol 1997; 21: 1123-30.

  10. 10.Jiménez R, Eble J, Reuter V, Epstein H, Folpe A. Concurrent angiomyolipoma and renal cell neoplasia: a study of 36 cases. Mod Pathol 2001; 14: 157-63.




2020     |     www.medigraphic.com