Urías EDM, González PMC, Rascón AA, Díaz RGÁ

Language: Spanish
References: 14
Page: 49-53
PDF size: 181.62 Kb.

ABSTRACT

Objective: Establish the clinical presentation of hemophagocytic syndrome in pediatric patients from the State of Sonora.
Materials and Methods: Chart analysis of patients with discharge diagnosis of hemophagocytic syndrome between the years of 2000 and 2011 in the Children’s Hospital of the State of Sonora.
Results: We studied 12 charts from which only 8 met both the inclusion and exclusion criteria. Mean age from the study was 7 years with a mean hospitalization of 3.8 days. All 100% of the patients met the Histiocyte Society Guidelines to be classified as hemophagocytic syndrome. 50% of the patients presented with epidemiological association for Rickettsia rickettsi infection which was classified post mortem as Rocky Mountains Spotted Fever.
Discussion: The diagnosis process requires a high suspicion index, but most of all, it must be considered in any patient with severe infections or proinflammatory conditions like neoplasm, infections or autoimmune disease that do not respond to regular therapy.

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