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2016, Number 2

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Revista Cubana de Obstetricia y Ginecología 2016; 42 (2)

From the embryological basis to the clinical Prune Belly syndrome

Pachajoa H

Language: Spanish
References: 9
Page: 254-259
PDF size: 246.63 Kb.


ABSTRACT

Prune Belly syndrome is a congenital disorder that is due, as currently reported, to genetic basis. It is characterized by the following triad: deficiency of abdominal muscles in varying degrees, bilateral cryptorchidism and urinary tract anomalies. Two variants of the syndrome are identified, a deadly one and another compatible with life.


REFERENCES

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  2. Greskovich FJ, Nyberg LM. The Prune Belly syndrome: A review of its etiology, defects, treatment and prognosis. J Urol. 1988;140:707-12.

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  4. OMIM Entry - # 100100 - Abdominal muscles, absence of, with urinary tract abnormality and cryptorchidism [Internet]. [Citado 2 de octubre de 2015]. Disponible en: http://www.omim.org/entry/100100.

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