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ISSN 1561-3062 (Electronic)

2016, Number 2

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Revista Cubana de Obstetricia y Ginecología 2016; 42 (2)

Anterior sacral meningocele simulating ovarian cyst baffled

Pérez TJE, Román RPA, García SI, Castillo AI, Bencomo RL, Marcos GY

Language: Spanish
References: 15
Page: 207-214
PDF size: 543.07 Kb.


ABSTRACT

The anterior sacral meningocele is a rare genetic anomaly associated with connective tissue diseases such as Marfan syndrome, Loeys-Dietz syndrome, neurofibromatosis type 1 and others. The aim of this paper is to present the case of a fetus with anterior sacral meningocele, initially diagnosed as a large multilobulated ovarian cyst in a patient diagnosed with Marfan syndrome It is a herniation of the dural sac, through large sacral foramina, and deformed by dural ectasia, occupying mostly by cerebrospinal fluid. Puncture or rupture these structures during surgery has been associated with serious complications and even death.


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