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ISSN 1684-1824 (Electronic)

2016, Number 5

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Rev Méd Electrón 2016; 38 (5)

Rutledge’s lip-glossopexy in a patient with Robin sequence. Case report

Del Busto GCM, Santana González-Chávez A, Calvo PD, Peñate SCO, López TO, Valhuerdi PC

Language: Spanish
References: 34
Page: 711-718
PDF size: 299.75 Kb.


ABSTRACT

The Robin sequence, previously known as Pierre Robin syndrome, is charaterized by the presence of micrognathia or retrognathia, glossoptosis with or without cleft palate. The newborns with this syndrome may present airway obstruction, feeding difficulties, growth retardation and chronic hypoxemia. Half of these patients have associated malformations. The incidence is almost 1: 8 500. The current options for the treatment of the airway obstruction in these patients range from prone position, nasofaringeal intubation, glossopexy with lip adhesion, mandibular distraction up to tracheostomy. We presented a variant of emergency surgical treatment carried out in a newborn having a Robin sequence with respiratory difficulty. A Routledge´s lip-glossopexy was made. The patient had a favorable post-surgery evolution in his ventilation and feeding.


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