Suárez BLC, Vargas VM, Simón BTI, Macías NMM, Carmenaty PA

Language: Spanish
References: 19
Page: 168-175
PDF size: 491.53 Kb.

ABSTRACT

A descriptive and retrospective study of the 22 dead with diagnosis of hemoglobin disease in the Hematology Service of "Dr. Juan Bruno Zayas Alfonso" Teaching General Hospital in Santiago de Cuba, was carried out from January, 2008 to December, 2012, aimed at identifying the clinical manifestations that caused fatal complications. In the series the icterus intensification prevailed as main cause of admission and the pulmonary thromboembolism, the infections and the hepatic failure as causes of death demonstrated by autopsy, although this was only carried out to the 22.7% of the dead; it was also observed that the survival curve began to decline starting from the 20 years in the male sex and from the 30 years in the female sex. The different causes of death were related to the progressive organic damage, so that the most affected organs were identified, to be able to establish preventive rules in the follow up of the patients with this disease, in order to minimize the vasooclusive crises that contribute to complications and early death.

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