Narváez PO, Reveles ZL, Serna SHI

Language: Spanish
References: 15
Page: 234-238
PDF size: 83.95 Kb.

ABSTRACT

Primary tumors in pulmonary arteries are uncommon, diagnosis being post mortem in more than 50% of the cases. This type of neoplasia is more frequent in adults, predominantly affects women in their 5th or 6th decade, is usually found in the trunk of the pulmonary artery and can spread to smaller arteries. This pathology is frequently misdiagnosed as chronic pulmonary thromboembolic disease, metastatic pulmonary neoplasm or idiopathic (primary) pulmonary hypertension, among other pathologies. The symptoms are usually nonspecific although most patients present with either dyspnea, chest pain, hemoptysis, systolic murmur and right-heart failure. A clinical case of a 51 year-old female patient with a one-year symptomatology is reported here. She was diagnosed chronic pulmonary embolism and was admitted to our hospital in April 1997, to undergo thromboendarterectomy. During surgery an infiltrative vascular tumor was found; the resection was difficult and the patient had important bleeding (5500mL) due to pulmonary artery damage. The patient had unsuccessful postoperative course and passed away due to hypovolemic shock. The hystopathologic report was a mesenchymal malignant tumor corresponding to a fibromyxosarcoma.

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