Thrombotic thrombocytopenic purpura secondary to systemic lupus erythematosus

Caridad Chao Pereira; Marianne Nievas Sánchez; Víctor Roca Campaña; Karen Valdés Alvarez

2015, Number 3

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Rev cubana med 2015; 54 (3)

Thrombotic thrombocytopenic purpura secondary to systemic lupus erythematosus

Chao PC, Nievas SM, Roca CV, Valdés ÁK

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Language: Spanish
References: 20
Page: 258-263
PDF size: 162.22 Kb.

ABSTRACT

Thrombotic thrombocytopenic purpura associated with systemic lupus erythematosus is very rare. One patient with prolonged febrile syndrome, polyarthralgia, headache, bilateral papilledema and behavioral changes is presented here. The clinical course, the imaging, laboratory and immunological studies that allowed the diagnosis of thrombotic thrombocytopenic purpura secondary to systemic lupus erythematosus are described. It was considered important to present this case by the infrequency with which the association of both entities also diagnosed because the diagnosis was a challenge for specialists and internal medicine residents.

REFERENCES

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Kwaan HC, Bennett CL. Thrombotic thrombocytopenic purpura. Semin Thromb Hemost. 2005;31:611-4.
De la Rubia C, Del Río G. Púrpura trombótica trombocitopénica. Med Clin (Barc). 2011;136(12):534-40.
Murria RJ, Murria JA. Thrombotic thrombocytopenic púrpura: Aetiology, pathophysiology and treatment. Blood Rev. 2006;20:51-60.
Burns ER, Lou Y, Pathak A. Morphologic diagnosis of thrombotic thrombocytopenic purpura. Am J Hematol. 2004;75:18.
Donadelli R, Orje JN, Capoferri C. Size regulation of von Willebrand factor–mediated platelet thrombi by ADAMTS13 in flowing blood. Blood. 2006;107:1943-50.
Binder WD, Traum AZ, Makar RS, Colvin RB. A 16 years old girl with confusion, anemia and thrombocytopenia. N Engl J Med. 2010;363;2352-61.
Bray VJ, West SG, Kristo DA. Simultaneous presentation of thrombotic thrombocytopenic purpura and systemic lupus erythematosus. South Med J. 1994;87:827-30.
Nesher G, Hanna VE, Moore TL, et al. Thrombotic microangiopathic hemolytic anemia in systemic lupus erythematosus. Semin Arthritis Rheum 1994;24:165-72.
Caramaschi P, Riccetti MM, Fratta Pasini A, et al. Systemic lupus erythematosus and thrombotic throm-bocytopenic purpura. Report of three cases and review of the literature. Lupus. 1998;7:37-41.
Moschcowitz E. An acute febrile pleiochromic anemia with hyaline thrombosis of the terminal arterioles and capillaries. Arch Intern Med. 1925;36:8-93.
Kwaan HC, Bennett CL. Thrombotic thrombocytopenic purpura. Semin Thromb Hemost. 2005;31:611-4.
De la Rubia C, Del Río G. Púrpura trombótica trombocitopénica. Med Clin (Barc). 2011;136(12):534-40.
Murria RJ, Murria JA. Thrombotic thrombocytopenic púrpura: Aetiology, pathophysiology and treatment. Blood Rev. 2006;20:51-60.
Burns ER, Lou Y, Pathak A. Morphologic diagnosis of thrombotic thrombocytopenic purpura. Am J Hematol. 2004;75:18.
Donadelli R, Orje JN, Capoferri C. Size regulation of von Willebrand factor–mediated platelet thrombi by ADAMTS13 in flowing blood. Blood. 2006;107:1943-50.
Binder WD, Traum AZ, Makar RS, Colvin RB. A 16 years old girl with confusion, anemia and thrombocytopenia. N Engl J Med. 2010;363;2352-61.
Bray VJ, West SG, Kristo DA. Simultaneous presentation of thrombotic thrombocytopenic purpura and systemic lupus erythematosus. South Med J. 1994;87:827-30.
Nesher G, Hanna VE, Moore TL, et al. Thrombotic microangiopathic hemolytic anemia in systemic lupus erythematosus. Semin Arthritis Rheum 1994;24:165-72.
Caramaschi P, Riccetti MM, Fratta Pasini A, et al. Systemic lupus erythematosus and thrombotic throm-bocytopenic purpura. Report of three cases and review of the literature. Lupus. 1998;7:37-41.