Portela-Ortíz JM, Hernández-Cortés C, Delgadillo-Arauz C, Alarcón-Rodríguez JJ

Language: Spanish
References: 10
Page: 122-124
PDF size: 139.00 Kb.

ABSTRACT

Myotonic dystrophy type 1 or Steinert’s disease is a progressive disease that manifests itself in late childhood or adulthood, and is characterized by muscle weakness, atrophy, as well as a marked muscle paralysis of mastication, neck, pharynx and thighs in its distal portion. During the perioperative management of patients with this disease it is not unusual the presentation of myotonias, respiratory depression, cardiac arrhythmias and residual neuromuscular blockade; the latter being the predisposing factor of postanesthetic complications that can lead to cardiac arrest. We report a patient who underwent a resection of a renal cyst in whom we use total intravenous anesthesia combined with the rocuronium-sugammadex binomial, achieving a complete reversal of the neuromuscular blockade and an absence of the residual block and postanesthesia complications. Thus, rocuronium-sugammadex appears to be a safe option in patients with Steinert’s disease requiring neuromuscular blockade.

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