2003, Number 3
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Med Cutan Iber Lat Am 2003; 31 (3)
Progressive Symmetric Erythrokeratodermia: Report of a Sporadic Case and of Late Appearance
Zanini M, Bertino D, Corrêa e Silva K, Camargo PLH, Landaman G, Freitas E
Language: Portugués
References: 14
Page: 192-194
PDF size: 162.73 Kb.
ABSTRACT
Authors relate a sporadic case of late appearance of progressive symmetric erythrokeratoderma and review the literature. It is a rare inherited cornification disorder, manifested by symmetrical hyperkeratotic plaques on an erythematous base generally over the extremities and buttocks, and with onset during first year of life.
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