Rojas R, Kaplan JD, Gordillo H, Mastrogiovanni L, Palacios E

Language: Spanish
References: 10
Page: 129-133
PDF size: 830.41 Kb.

ABSTRACT

Fibrous dysplasia is a benign idiopathic skeletal disorder. It represents 2.5% of all bone tumors and 7.5% of benign bone tumors and presents a monostotic and polyostotic variant. Computerized Tomography is the gold standard imaging method for diagnosis and follow-up.
Surgical treatment is only necessary in cases of vessels and nerves entrapment or due to cosmetic reason secondly to bone deformity. Malignant transformation occurs in only 1% of cases involving mostly the skull and facial bones. Differential diagnosis includes Paget disease, metastatic bone lesions and osteofibrous dysplasia.
McCune Albright syndrome should be distinguished from Neurofibromatosis.

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