2014, Number 3
Schwannoma of the median nerve in a patient with neurofibromatosis type I
Ramos-Cárdenas R, Acevedo-Estrada RI, Pineda-Villafuerte EF
Language: Spanish
References: 12
Page: 371-374
PDF size: 448.71 Kb.
ABSTRACT
Peripheral nerve tumors are rare, in hand represents 1%. There are two types 1) schwannoma or neurilemmoma and 2) neurofibromas. Schwannomas are encapsulated, ovoid, firm, benign tumors originated from Schwann cells. Neurilemmoma. Usually occur between 30-60 years of age, regardless of sex or race; 45% are in head/neck, 19% upper limb, and lower limb 13.5%, the palmar surfaces are more commonly affected than, may be multiple. They present as slow-growing tumors, alone, with or without associated neurologic disease. Usually asymptomatic, inflammation rarely disturbs nerve function, but paresthesia or hyperesthesia may occur. If tumor is palpable it can move in transverse direction. The Multiple schwannomas are rare, but can occur in neurofibromatosis type 2 or schwannomatosis. The diagnosis is hard and often done during surgery or histopathological examination. In the Ambulatory Surgery Center, ISSSTE; a case of a 36-year-old presented with a diagnosis of Neurofibromatosis type 1 or Von Recklinghausen disease was presented. Tumor in the distal third of the right forearm anterior surface, 5cm diameter, soft, non-mobile, fixed to deep planes, not painful, unaltered sensitivity, strength 4/5, slow-growing progressive. Is scheduled for surgery, intraoperative tumor depending right median nerve, covering entire thickness of the nerve, schwannoma observed diagnosis is made, closure of the wound is determined. The patient progressed satisfactorily retaining the function of the affected nerve. Conclusion. Any tumor nerve should think of schwannoma, diagnosing earlier during surgery, in order not to cut the involved nerve, and thus allow long-term function either motor and/or sensory.REFERENCES