2005, Number 4
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Med Sur 2005; 12 (4)
Evans syndrome
Vázquez EG, Aguilar DC
Language: Spanish
References: 22
Page: 216-219
PDF size: 45.80 Kb.
ABSTRACT
A case of a 40 year old male patient with a 7 day history of hemolytic anemic syndrome (anemia plus direct Coombs test positive) with thrombocytopenia and neutropenia is presented. The case was studied as in-patient at the department of Internal Medicine of our hospital. The diagnosis was Evans' syndrome in coexistence with a possible Vitamin B12 deficiency. In the present report we discussed this entity.
REFERENCES
Evans RS, Takahashi K, Duane RT, Payne R, Liu C. Primary thrombocytopenic purpura and acquired hemolytic anemia; evidence for a common etiology. AMA Arch Intern Med 1951; 1: 48-65.
Mathew, Prasad. Evans Syndrome en http://www.emedicine.com/. 25 de Octubre de 2005.
Mathew P, Chen G, Wang W. Evans' syndrome: results of a national survey. J Pediatr Hematol Oncol 1997; 5: 433-7.
Savasan S, Warrier I, Ravindranath Y. The spectrum of Evans’ syndrome. Arch Dis Child 1997; 77: 245-248.
de Quiros JF, Pinto V, Hevia S, Vigon R. Immune complex-mediated hemolytic anaemia and Evans' syndrome induced by diclofenac. Vox Sanguinis 1997; 72: 121-3.
Keung Y, Mallarino MC, Cobos E. Drug-induced Evans' syndrome. Ann Intern Med 1998; 4: 327.
Ucci G, Ferrando P, Valentini D, Zavallone L. A case of Evans’ syndrome in a patient with ulcerative colitis. Dig Liver Dis 2003; 6: 439-41.
Knecht H, Baumberger M, Tobon A, Steck A. Sustained remission of CIDP associated with Evans' syndrome. Neurology 2004; 4: 730-2.
Kakaiya RM, Sherman LA, Miller WV, Katz AJ. Nature of platelet antibody in Evans' syndrome: a case report. Ann Clin Lab Sci 1981; 6: 511-5.
Avcin T, Jazbec J, Kuhar M et al. Evans' syndrome associated with antiphospholipid antibodies. J Pediatr Hematol Oncol 2003; 9: 755-6.
Font J, Jimenez S, Cervera R, Garcia-Carrasco M, Ramos-Casals M, Campdelacreu J, Ingelmo M. Splenectomy for refractory Evans’ syndrome associated with antiphospholipid antibodies: report of two cases. Ann Rheum Dis 2000; 11: 920-3.
Keung YK, Cobos E, Bolanos-Meade J, Issarachai S, Brideau A, Morgan D. Evans syndrome after autologous bone marrow transplant for recurrent Hodgkin’s disease. Bone Marrow Transplant 1997; 12: 1099-101.
Wang W, Herrod H, Pui CH, Presbury G, Wilimas J. Immunoregulatory abnormalities in Evans' syndrome. Am J Hematol 1983; 4: 381-90.
Teachey DT, Manno CS, Axsom KM, Andrews T, Choi JK, Greenbaum BH, McMann JM, Sullivan KE, Travis SF, Grupp SA. Unmasking Evans' syndrome: T-cell phenotype and apoptotic response reveal autoimmune lymphoproliferative syndrome (ALPS). Blood 2005; 6: 2443-8. Epub 2004 Nov 12.
Blanchette VS, Kirby MA, Turner C. Role of intravenous immunoglobulin G in autoimmune hematologic disorders. Semin Hematol 1992; 3 Suppl 2: 72-82.
Raetz E, Beatty PG, Adams RH. Treatment of severe Evans' syndrome with an allogeneic cord blood transplant. Bone Marrow Transplant 1997; 5: 427-9.
Duperier T, Felsher J, Brody F. Laparoscopic splenectomy for Evans' syndrome. Surg Laparosc Endosc Percutan Tech 2003; 1: 45-7.
Galor A, O’Brien T. Rituximab treatment for relapsed autoimmune hemolytic anemia in Evans' syndrome. Int J Hematol 2003; 4: 335-6.
Ramanathan S, Koutts J, Hertzberg MS. Two cases of refractory warm autoimmune hemolytic anemia treated with rituximab. Am J Hematol 2005; 2: 123-6.
Zecca M, Nobili B, Ramenghi U, Perrotta S, Amendola G, Rosito P, Jankovic M, Pierani P, De Stefano P, Bonora MR, Locatelli F. Rituximab for the treatment of refractory autoimmune hemolytic anemia in children. Blood 2003; 10: 3857-61. Epub 2003 Jan 16.
Shanafelt TD, Madueme HL, Wolf RC, Tefferi A. Rituximab for immune cytopenia in adults: idiopathic thrombocytopenic purpura, autoimmune hemolytic anemia, and Evans' syndrome. Mayo Clin Proc 2003; 11: 1340-6.
Galindo M, Khamashta MA, Hughes GR. Splenectomy for refractory thrombocytopenia in the antiphospholipid syndrome. Rheumatology (Oxford) 1999; 9: 848-53.