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2005, Number 2

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Gac Med Mex 2005; 141 (2)

Proximal pancreatectomy in a case of nesidioblastosis.

Flores-Alvarado LJ, Sánchez ES, Zepeda MA, Ramírez-Garcial SA, Bueno-Topete MR, Ayub-Ayala M, Vázquez-López LS, Gallardo-Meza A, Nuño-Moren P, Gaspar-Barba CE

Language: Spanish
References: 14
Page: 157-160
PDF size: 101.40 Kb.


ABSTRACT

A 19 month-old child who presented seizures secondary to intractable hypoglycemia, fulfilling the clinical and biochemical criteria for hyperinsulinism was studied. Histopathological findings of the pancreas showed the presence of small clusters of b cell islets throughout acinar tissue near ducts, in both the head and the proximal third of the body. Proximal pancreatectomy (60%) and distal pancreatic-jejunostomy (Roux-in-Y) were performed. This procedure was effective in reverting hypoglycemia and constitutes the first successful alternative treatment.


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