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ISSN 1561-3070 (Electronic)

2013, Number S1

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Rev Cub Oftal 2013; 26 (S1)

Syndrome of myelinated retinal nerve fibers, myopia and amblyopia

López FD, Méndez STJ

Language: Spanish
References: 48
Page: 668-678
PDF size: 214.89 Kb.


ABSTRACT

The intraocular myelin fibers emerge since one's birth and it is usually located around the papilla. The syndrome of myelinated retinal nerve fibers was described for the first time by Virchow in 1856. This appears in the form of grooved patches, white or grayish white with imprecise and feathery borders following a coincident configuration with the distribution of the retinal nerve fibers. A four years-old girl who was taken to the doctor's office because she presented with right eye deviation. In the ophthalmologic exam, the best corrected visual acuity was 0.1 and the ophthalmoscopy confirmed myelinated retinal nerve fibers. Myopia and amblyopia were often associated in these patients. In spite of the poor visual results and the lack of other available therapies, specialists tend to apply aggressive treatment for amblyopia, although this procedure is still controversial in the medical literature.


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