2013, Number 5
<< Back
Rev Mex Neuroci 2013; 14 (5)
Fibrous dysplasia of the skull: case report and literature review
Díaz CA, Zottis GC, Castillo TV, Rehder R, Borba LAB
Language: Spanish
References: 14
Page: 286-290
PDF size: 782.90 Kb.
ABSTRACT
Fibrous dysplasia consists of benign skeletal disorder present especially in adolescents and young adults, characterized by abnormal fibrous proliferation with normal or immature bone, located either in a single bone or affecting in a diffuse form the skeletal. Face and skull are affected in approximately 10-25% of the patients presenting fibrous dysplasia in a monostotic form and approximately 50% of patients presenting polyostotic form of the disease. Fibrous dysplasia may manifest in several forms and radiological and computerized tomographies are essential as complementary exams to determine the extension of such lesions. Literature review suggests surgical resection as a possible treatment, especially in those patients presenting cosmetic deformity and functional complications. Due to its benign evolution, surgery consists in preserving the function of the system taken by the lesion. We report the case of a patient presenting fibrous dysplasia in fronto-parietal bone submitted to surgical intervention in Evangelic University Hospital of Curitiba.
REFERENCES
Pruksakorn P, Shuangshoti S, Siwanuwatn R, Lerdlum S, Sunthornvothin S, Snabboon T: Craniofacial Fibrous Dysplasia. Inter Med 2000; 49: 249-50.
Atalar M, Ozum U: Monostotic fibrous dysplasia of the clivus: imaging findings. Turkish Neurosurgery 2010; 20(1): 77-81.
Lee JS, Fitzgibbon E, Butman JA, Dufresne CR, Kushner H, Wientroub S, Robey PG, Collins MT. Normal vision despite narrowing of the optic canal in fibrous dysplasia. N Engl J Med 2002; 347(21): 1670-6.
Buraczewski J, Dabska M. Pathogenesis of aneurismal bone cystrelationship between the aneurysmal bone cyst and fibrous dysplasia of bone. Cancer 1970; 28: 597-604.
Feiring W, Feiring EH, Davidoff LM. Fibrous dysplasia of the skull- General aspects of fibrous dysplasia. J Neurosurg 1951; 8(4): 377-93.
Scott M, Peale AR, Croissant PD. Intracranial midline anterior fossae ossifying fibroma invading orbits, paranasal sinuses, and right maxillary antrum. J Neurosurg 1971; 34: 827-31.
Dumont AS, Boulos PT, Jane JAJr, Ellegala DB, Newman SA, Jane JA. Cranioorbital fibrous dysplasia: with emphasis on visual impairment and current surgical management. Neurosurg Focus 2001; 10(5): 1-8.
Michael CB, Lee AG, Patrinley JR, Stal S, Blacklock JB. Visual loss associated with fibrous dysplasia of the anterior skull base. J Neurosurg 2000; 92: 350-4.
Mortensen A, Bojsen-Moller M, Rasmussen P. Fibrous dysplasia of the skull with acromegaly and sarcomatous transformation. J Neuro- Oncology 1989; 7: 25-9.
Huvos AG, Higinbotham NL, Miller TR. Bone sarcomas arising in fibrous dysplasia. J Bone Joint Surg Am 1972; 54: 1047-56.
Ruggieri P, Sim FH, Bond JR, Unni KK. Maliganacies in fibrous dysplasia. Cancer 1994; 73(5): 1411-24.
Moser RP, Kransdorf MJ, Gilkey FW. Fibrous dysplasia. RadioGraphics 1990; 10(3): 519-37.
Chong VFH, Khoo JBK, Fan YF. Fibrous dysplasia involving the base of the skull. AJR 2002; 178: 717-20.
Lustig LR, Holliday MJ, McCarthy EF, Nager GT. Fibrous dysplasia involving the skull base and temporal bone. Arch Otolaryngol Head Neck Surg 2001; 127: 1239-47.