2013, Number 04
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MediSan 2013; 17 (04)
Abdominal aortic iliac aneurysms and Loeys-Dietz syndrome
Ortiz LD, Sánchez GD, Chércoles CL
Language: Spanish
References: 9
Page: 732-737
PDF size: 105.91 Kb.
ABSTRACT
The case report of a 29 year-old patient, with a history of aortic ectasia who had been
studied when she was 18 years through cineangiography is presented and a fusiform
aneurysm of the infrarrenal abdominal aorta and of the left primitive iliac artery, of
unspecific cause was found, which were substituted with left aortofemoral bypass. Later
on, in 2012, she presented pain and increase of the volume in the left inguinal region,
reason why she was assisted in the emergency room of "Saturnino Lora Torres" Teaching
Provincial Clinical Surgical Hospital in Santiago de Cuba, and evaluated by specialists of
the Angiology and Vascular Surgery Service, which determined to treat her with an
emergency surgery, when observing an anastomotic aneurysm of the left femoral artery
of fungal cause, and the characteristics: craneosinostosis, bifid uvula and cleft palate;
characteristic of Loeys Dietz syndrome.
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