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Órgano Oficial de la Sociedad Mexicana de Angiología y Cirugía Vascular

2011, Number 1

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Rev Mex Angiol 2011; 39 (1)

Disección aórtica y embarazo

Uribe G, Sigler L, Jiménez R, Romero C, Paipilla O

Language: Spanish
References: 30
Page: 33-38
PDF size: 424.85 Kb.


ABSTRACT

Introduction: Aortic dissection is rare. It may affect the thoracic or even the abdominal segment with rupture or obstruction of important branches. When it occurs during pregnancy there is the risk of maternal and fetal death.
Objective: To present two pregnant patients with Marfan´s syndrome that had dissection of the aorta with severe complications.
Material and methods: A 26-year-old woman with a 28 week pregnancy had a sudden convulsion, loss of consciousness, right hemiplegia and pulsesless low extremities. Another 22 year-old woman with family history of Marfan´s, 34 weeks of the first pregnancy had loss of conscience and sudden death after a shower in her house.
Results: After the first patient was evaluated by a multispecialty group it was concluded that she was too ill to have any thoracic procedure, thus a cesarean section for a death fetus and fenestration of the suprarenal aorta were done with full maternal recovery. The second patient was declared death at her house and autopsy showed acute dissection of the aortic arch with approximately 1,500 cm3 intramural and pericardial hematoma and a death fetus.
Conclusions: Clinical characteristics of pregnant patients with Marfan´s syndrome must be studied and treated by their gynecologist, then be referred to a cardiologist who after evaluating the condition may suggest medical, surgical or endovascular procedures.


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