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ISSN 0210-5187 (Electronic)

2013, Number 1

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Med Cutan Iber Lat Am 2013; 41 (1)

Reticular hemangioma of the lower extremity associated with congenital structural anomalies: therapeutic approach

Morais P, Magina S, Reis A, Pinto H, Amil DJ, Rodrigues M, Silva G, Azevedo F, Guimarães H

Language: English
References: 21
Page: 38-42
PDF size: 217.12 Kb.


ABSTRACT

Reticular hemangioma is a recently described variant of infantile hemangioma that has a predilection for the lower extremity and perineum. It is often associated with recalcitrant ulceration, ano-genito-urinary-sacral anomalies, and rarely with cardiac overload. A premature newborn female presented with patchy, network-like cutaneous staining of the left lower limb, buttocks and perineum, prominent lateral venous dilations of the involved limb, dysmorphic external genitalia and imperforate anus. MRI revealed imperforate anus, rectovestibular fistula, coccygeal hypoplasia, medullary syringomyelic cavity and retroperitoneal hemangiomatous involvement. The clinical and imaging features were those of reticular hemangioma and ventral-caudal anomalies. The authors describe the therapeutic approach of this patient and the efficacy of vacuum-assisted closure of a large intractable ulceration.


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