2001, Number 3
<< Back Next >>
Arch Cardiol Mex 2001; 71 (3)
Congenital mitral stenosis 1991-2001 experience
Alva C, González B, Meléndez C, Jiménez S, Jiménez D, David F, Sánchez A, Ortegón J, Ledesma M, Magaña JA, Argüero R
Language: Spanish
References: 16
Page: 206-213
PDF size: 208.92 Kb.
ABSTRACT
Objective: To describe ten years of experience with congenital mitral stenosis.
Method: All cases with congenital mitral stenosis from January 1991 to 2001 were analized.
Results: 16 patients with congenital mitral stenosis were found, mean age 3 ± 3.08 years.
Types of obstructions: mitral commisures combined with tendinous cords fusion (45%), parachute mitral valve 37%, supravalvar mitral ring in one, fusion between papillary muscle and leaflets in one, and double mitral orifice in one. Hemodynamic (in mmHg) findings: wedge pressure 18.4 ± 4, pulmonary artery systolic 61 ± 21, diastolic 34 ± 15, mean 47 ± 18 mmHg, mean transvalvar gradient (MTG) 12.9 ± 7.3, PRU 5.5 ± 3.8. Four patients received medical treatment. Surgical results: Six patients underwent mitral repair, and four were subjected to mitral valve replacement (two with previous mitral repair). Global mortality was 2 (12.5%). Follow-up was 3.5 ± 3 years. There was a significant difference when the initial MTG 22.6 ± 11.5 mmHg before surgical repair was compared with the final MTG 4.75 ± 1.5 (P‹ 0.05), also when initial MTG 12 ± 2.3 before mitral valve replacement was compared with the final MTG 6 ± 1.15 mmHg (P‹ 0.05).
Conclusion: Most patients are candidates for mitral surgical repair, however at mid term one third will require mitral valve replacement.
REFERENCES
Carpentier A: Congenital malformations of the mitral valve. In: Stark J, de Leval M, eds. Surgery for congenital heart defects. Londres: Grune and Stratton 1994; 599-614.
Daoud G, Kaplan S, Perrin EV, Dorst J, Edwards F: Congenital mitral stenosis. Circulation 1963; 27: 185-196.
Ruckman R, Van Praagh R: Anatomic types of congenital mitral stenosis: report 49 autopsy cases with consideration of diagnosis and surgical implications. Am J Cardiol 1978; 42: 592-601.
Strasburger J. Congenital mitral valve disease. In: Garzon A, Bricker JT, McNamara D, eds. The Science and Practice of Pediatric Cardiology. Philadelphia, Lea & Febiger 1990; 1308-1315.
Shone JD, Sellers RD, Anderson RC, Adams P, Lillehei CW, Edwards JE: The developmental complex of “parachute mitral valve”, supravalvular ring of the left atrium, subaortic stenosis and coarctation of aorta. Am J Cardiol 1963; 11: 714-725.
Grifka RG, O’laughlin MP, Nihill MR, Mullins CE: Double transeptal double-ballon valvuloplasty for congenital mitral stenosis. Circulation 1992; 85: 123-129.
Zias EA, Mavroudius C, Backer CL, Kohr LM, Gotteiner NL, Rocchini AP: Surgical repair of the congenitally malformed mitral valve in infants and children. Ann Thorac Surg 1998; 66: 1551-1559.
Chauvaud SM, Milhaleanu SA, Gaer JAT, Carpentier AC: Surgical treatment of congenital mitral valve stenosis: The Hospital Broussais experience. Cardiol Young 1997; 7:15-21.
Kadoba K, Jonas RA, Mayer JE, Castañeda AR: Mitral valve replacement in the first year of life. J Thorac Cardiovasc Surg 1990; 100: 762-768.
van Doorn C, Yates R, Tsang V, de Leval M, Elliot M: Mitral valve replacement in children: mortality, morbidity and haemodinamic status up to medium term follow up. Heart 2000; 84: 636-642.
Ledesma Velasco M, Solorzano Zepeda F, David Gómez F, Alva Espinoza C, Montoya Guerrero SA, Antezana Castro J, et al: Percutaneous mitral commisurotomy with an Inoue catheter in congenital mitral stenosis. Arch Inst Cardiol Mex 1995; 65: 261-263.
Coles JG, Williams WG, Watanabe T, Sherret H, Dasmahapalva HK, Freedom RM, et al: Surgical experience in patients with congenital mitral valvular anomalies. Circulation 1987; 76 (Supp III): 117-122.
Adatia I, Moore PH, Jonas R, Colan S, Lock JM, Keane JF: Clinical course an hemodynamic observations after supraannular mitral valve replacement in infants and children. J Am Coll Cardiol 1997; 29:1089-1094.
Sullivan ID, Robinson PJ, de Leval M, Graham TP: Membranous supravalvular mitral stenosis: a treatable form of congenital heart disease. J Am Coll Cardiol 1986; 8: 159-164.
Alday L, Juaneda E: Percutaneous ballon dilation in congenital mitral stenosis. Br Heart J 1987; 57: 479-482.
Spevak P, Bass J, Ben-Shachar G, Hesslein P, Keane J, Perry S, et al: Ballon angioplasty for congenital mitral stenosis. Am J Cardiol 1989; 66: 472-476.